English
 附属病院
 輸血部
 
教授
松本   雅則
Matsumoto Masanori

リポジトリへのリンク

研究分野
血液内科学 

キーワード
血液内科学 

研究テーマ
フォンビルブランド因子特異的切断酵素(ADAMTS13)  フォンビルブランド因子,プロテアーゼ   
血栓性微小血管障害症(TMA)  ADAMTS13, von Willebrand因子    TMAのVWFとADAMTS13による解析。

著書
Chapter 5. Hereditary deficiency of ADAMTS13 activity – Upshaw-Schulman syndrome. ADAMTS13 book  2015  Springer (edited by George Rodgers)  73-90  Fujimura Y, Kokame K, Yagi H, Isonishi A, Matsumoto M, Miyata T     
Crucial Role of ADAMTS13 Related to Endotoxemia and Subsequent Cytokinemia in the Progression of Alcoholic Hepatitis.  2012  INTech  Chapter 10  Uemura M, Fujimura Y, Matsuyama T, Matsumoto M, Takaya H, Morioka C, Fukui H.     
Thrombotic microangiopathy. Recent Advances in Thrombosis and Hemostasis.  2008  Springer-Verlag  625-639  Fujimura Y, Matsumoto M, Yagi H.     
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論文
Poor-responder to plasma exchange therapy in acquired TTP is associated with ADAMTS13 inhibitor boosting: Visualization of an ADAMTS13-inhibitor complex, and its proteolytic clearance from plasma.  Isonishi A, Bennett CL, Plaimauer B, Scheiflinger F, Matsumoto M, Fujimura Y.  Transfusion  学術雑誌  共著  in press  2015       
A Novel Quantitative Hemolytic Assay Coupled with Restriction Fragment Length Polymorphisms Analysis Enabled Early Diagnosis of Atypical Hemolytic Uremic Syndrome and Identified Unique Predisposing Mutations in Japan.  Yoshida Y, Miyata T, Matsumoto M, Shirotani-Ikejima H, Uchida Y, Ohyama Y, Kokubo T, Fujimura Y.  PLoS ONE  学術雑誌  共著  10/ 5, e0124655  2015    10.1371   
A rapid, fully automated and highly sensitive ADAMTS13 gold particle immunoassay using a routine biochemistry analyser.  Kato S, Tanaka M, Isonishi A, Matsumoto M, Samori T, Fujimura Y.  Br J Haematol  学術雑誌  共著  in press  2015       
Autoimmune-type atypical hemolytic uremic syndrome treated with eculizumab as first-line therapy.  Hisano M, Ashida A, Nakano E, Suehiro M, Yoshida Y, Matsumoto M, Miyata T, Fujimura Y, Hattori M.  Pediatr Int  学術雑誌  共著  57/ 2, 313-317  2015/04    10.1111/ped.12469.   
STEC:O111-HUS complicated by acute encephalopathy in a young girl was successfully treated with a set of hemodiafiltration, steroid pulse, and soluble thrombomodulin under plasma exchange.  Yada N, Fujioka M, Bennett C, Inoki K, Miki T, Watanabe A, Yoshida T, Hayakawa M, Matsumoto M, Fujimura Y.  Clinical Case Reports  学術雑誌  共著  3/ 4, 208-212  2015/04    10.1002/ccr3.196   
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